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Congenital Long QT Syndrome | Kraemer Academy (qtc.mocha.app)

Congenital Long QT Syndrome | Kraemer Academy (qtc.mocha.app)

Congenital Long QT Syndrome (LQTS) is an inherited channelopathy characterized by prolongation of the QT interval on the ECG and a predisposition to malignant ventricular arrhythmias, particularly torsades de pointes, which may cause syncope, seizures, or sudden cardiac death in individuals with structurally normal hearts.

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